One Case of the Progressive Muscular Dystrophy

A Case of Progressive Muscular Dystrophy

(1) The method of attaining the erect position, similating the climbing method of the Aran Duchenne type. (2) No wasting of the muscles of the hands. Hypertrophy of the biceps in places. (3) The talipes position of the feet, (clawfoot). (4) The position of the back. (Myopathic lordosis). G. M., age 23. Unmarried. Kalat State. Family History.?Father alive, healthy. Mother died after one month's ...

[Progressive muscular dystrophy].

This paper describes the case of a young man with progressive muscular dystrophy who had supraventricular arrhythmias and intractable congestive failure. Hemodynamic studies and left cineventriculographic findings were compatible with a diagnosis of severe left ventricular failure. Coronary cinearteriography showed an abrupt ending of the artery to the sino-atrial node. At necropsy, a noninflam...

Progressive Muscular Dystrophy (Erb.)

[A case of progressive muscular dystrophy with hypertrophic cardiomyopathy].

概 要 症例 は40才,男 性.7才 頃 か ら上・下 肢 の萎 縮 な らび に筋 力低 下 が出現 し,20才 頃 か ら 歩 行不 能 とな った.進 行 が 比較 的緩 徐 で あ る こ とか らBecker型 筋 ジ ス トロフ ィー と診 断 した. 心 工コ 一,心 臓 カテ ー テル 検査 の結果,心 室 中 隔の非 対 称性 肥 大 が認 め られ,右室 生 検 心筋 像 も典型 的 な肥 大 型心 筋症(HCM)の 所 見 に一致 した.一 般 に筋 ジ ス トロフ ィー に拡 張 型 心筋症 (DCM)様 の心筋 障 害 を合 併 す る こ とは よ く知 られ て お り,特 にDuchenne型 でそ の頻 度 が 高 い.一 方,Duchenne型 の 良性 型 とも言 え るBecker型 に心病 変 を合 併 す る こ とは まれ と され て ...

The electrocardiogram in Duchenne progressive muscular dystrophy.

Interpretation of the electrocardiogram in the Duchenne form of progressive muscular dystrophy (PMD) is still debated in the literature. The group studied consisted of 106 patients with the Duchenne type of PMD, aged 3 to 29 years. The duration of the disease varied from a few months to 15 years. One hundred one patients had abnormal electrocardiograms. These were of four types: type a (64 case...